FITC标记的亚硫酸盐氧化酶抗体
产品名称： FITC标记的亚硫酸盐氧化酶抗体
英文名称： Anti-Sulfite oxidase/FITC
产品编号： HZ-10426R-FITC
产品价格： null
产品产地： 中国/上海
品牌商标： HZbscience
更新时间： 2023-08-17T10:24:20
使用范围： ICC=1:50-200 IF=1:50-200
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Rabbit Anti-Sulfite oxidase/FITC Conjugated antibody
FITC标记的亚硫酸盐氧化酶抗体
| 英文名称 | Anti-Sulfite oxidase/FITC |
| 中文名称 | FITC标记的亚硫酸盐氧化酶抗体 |
| 别 名 | SO; EC 1.8.3.1; mitochondrial; Sulfite oxidase; Sulfite oxidase mitochondrial; Sulfite oxidase, mitochondrial precursor; Suox; SUOX_HUMAN. |
| 规格价格 | 100ul/2980元 购买 大包装/询价 |
| 说 明 书 | 100ul |
| 研究领域 | 肿瘤 细胞生物 神经生物学 信号转导 转录调节因子 新陈代谢 线粒体 |
| 抗体来源 | Rabbit |
| 克隆类型 | Polyclonal |
| 交叉反应 | |
| 产品应用 | ICC=1:50-200 IF=1:50-200 not yet tested in other applications. optimal dilutions/concentrations should be determined by the end user. |
| 分 子 量 | 52kDa |
| 性 状 | Lyophilized or Liquid |
| 浓 度 | 1mg/ml |
| 免 疫 原 | KLH conjugated synthetic peptide derived from human Sulfite oxidase |
| 亚 型 | IgG |
| 纯化方法 | affinity purified by Protein A |
| 储 存 液 | 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol. |
| 保存条件 | Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C. |
| 产品介绍 | background: Sulfite oxidase is a homodimeric protein localized to the intermembrane space of mitochondria. Each subunit contains a heme domain and a molybdopterin-binding domain. The enzyme catalyzes the oxidation of sulfite to sulfate, the final reaction in the oxidative degradation of the sulfur amino acids cysteine and methionine. Sulfite oxidase deficiency results in neurological abnormalities which are often fatal at an early age. Alternative splicing results in multiple transcript variants encoding identical proteins. [provided by RefSeq, Jul 2008] Subunit: Homodimer. Subcellular Location: Mitochondrion intermembrane space. DISEASE: Defects in SUOX are the cause of isolated sulfite oxidase deficiency (ISOD) [MIM:272300]; also known as sulfocysteinuria. ISOD is characterized by neurological abnormalities including multicystic leukoencephalopathy with brain atrophy. Patients often suffer from seizures. Often leads to death at an early age. Similarity: Contains 1 cytochrome b5 heme-binding domain. Database links: Entrez Gene: 6821 Human Entrez Gene: 211389 Mouse Omim: 606887 Human SwissProt: P51687 Human SwissProt: Q8R086 Mouse Unigene: 558403 Human Unigene: 23352 Mouse Important Note: This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications |
亚硫酸盐氧化酶是一种定位于线粒体膜间空间的同源二聚体蛋白。每个亚基包含一个血红素结构域和一个钼卟啉结合结构域。该酶催化亚硫酸盐氧化成硫酸盐，最后氧化降解硫氨基酸半胱氨酸和蛋氨酸。亚硫酸盐氧化酶缺乏导致神经系统异常，这在早年常常是致命的。选择性剪接导致编码相同蛋白质的多个转录变体。[ RefSeq，JUL 2008 ]